Russian Federation
Russian Federation
Russian Federation
Actually the screening of all the known genes allows identifying mutations only in 60– 65% patients with arrhythmogenic right ventricular dysplasia. This review analyses domestic and foreign studies on this issue on a basis of long-term observation. The materials presented demonstrate problems of the genotype-specific diagnostics and prompt treatment of the patients with this disease
arrhythmogenic right ventricular dysplasia, sudden cardiac death, ventricular tachycardia, cardioverter defibrillator, radiofrequency ablation, family screening.
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